Interv Akut Kardiol. 2023;22(4):173-179 | DOI: 10.36290/kar.2023.029

Arrhythmias in patients with adult congenital heart disease

Ondřej Toman^{1, 3}, Tomáš Zatočil^{1, 3}, Lumír Koc^{1, 3}, Daniela Žáková^{2, 3}, Martin Fiala^{1, 3}

¹ Interní kardiologická klinika FN Brno a LF MU Brno

² Centrum kardiovaskulární a transplantační chirurgie Brno

³ Centrum komplexní péče o vrozené srdeční vady v dospělosti, Brno

Arrhythmias are among the most frequent and serious complications in patients with adult congenital heart disease. The arrhythmogenic substrate is specific for different congenital heart diseases, either due to congenital anatomical malformations or as a result of surgical repair. Given the often borderline haemodynamic status, rhythm-control therapy is preferred, including the use of interventional methods (catheter ablation, pacemaker/cardioverter implantation, resynchronisation therapy). Periodic and thorough risk stratification is essential in the prophylaxis of sudden cardiac death. Patients with arrhythmias and severe congenital heart disease should be managed and treated in superspecialised expert centres. The aim of this article is to review the recent knowledge and guidelines for the care of these patients.

Keywords: arrhythmias, adult congenital heart disease, sudden cardiac death, catheter ablation, ICD implantation.

Received: March 30, 2023; Revised: October 31, 2023; Accepted: November 3, 2023; Published: November 28, 2023  Show citation