Interv Akut Kardiol. 2004;3(2):79-82

BRUGADA SYNDROME AS A RISK OF SUDDEN CARDIAC DEATH

Sabina Krištofová, Karel Dvořák
II. interní oddělení kardiovaskulární, Městská nemocnice, Ostrava

Brugada syndrome is a mostly inherited arrhytmogenic disease chracterized by the typical ECG patterns of ST-segment elevation in leads V1-3 often with incomplete right bundle-branch block, and an increased risk of sudden cardiac death as a result of ventricular fibrillation.

In this summary article, the occurence of this syndrome, electrocardiografic diagnosis, ST- segment changes during ajmaline test, electrophysiological studies, prognosis and the possibilities of the treatmen is dealt with. It is an emphasized necessity of early diagnosis for correct examination and treatment of patients with Brugada syndrome.

Keywords: Brugada syndrome, sudden cardiac death, ST-segment elevation, test with ajmalin.

Published: December 31, 2004  Show citation

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Krištofová S, Dvořák K. BRUGADA SYNDROME AS A RISK OF SUDDEN CARDIAC DEATH. Interv Akut Kardiol. 2004;3(2):79-82.

Brugadův syndrom je většinou dědičné arytmogenní onemocnění charakterizované typickým nálezem elevací ST úseku ve svodech V1-3 často s obrazem inkompletní blokády pravého raménka Tawarova a zvýšeným rizikem náhlé srdeční smrti podmíněné komorovou fibrilací.

Autoři v přehledném článku pojednávají o výskytu, elektrokardiografické diagnostice, změnách ST úseku při testování s ajmalinem, elektrofyziologickém vyšetření, prognóze a léčebných možnostech tohoto syndromu. Zdůrazňují nutnost časné diagnostiky pro adekvátní vyšetření a léčbu nemocných.

BRUGADA SYNDROME AS A RISK OF SUDDEN CARDIAC DEATH

Brugada syndrome is a mostly inherited arrhytmogenic disease chracterized by the typical ECG patterns of ST-segment elevation in leads V1-3 often with incomplete right bundle-branch block, and an increased risk of sudden cardiac death as a result of ventricular fibrillation.

In this summary article, the occurence of this syndrome, electrocardiografic diagnosis, ST- segment changes during ajmaline test, electrophysiological studies, prognosis and the possibilities of the treatmen is dealt with. It is an emphasized necessity of early diagnosis for correct examination and treatment of patients with Brugada syndrome.

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