Interv Akut Kardiol. 2015;14(4):154-157

Isolated form of left ventricular non compaction cardiomyopathy (LVNC) as a rare cause of heart failure

Sotiris Skopoulis1, Nikol Suková2, Petr Frídl3, Zarina Karimova4
1 Kardiologie na Bulovce s.r.o., Praha
2 Kardiocentrum Krajské nemocnice Liberec, Liberec
3 Kardiologie na Bulovce s.r.o., Praha
4 Klinika infekčních, parazitárních a tropických nemocí Nemocnice Na Bulovce, Praha

Left ventricular non-compaction cardiomyopathy (LVNC) is a rare, hereditary disease manifested by heart failure, tromboembolic complications

and arrhythmias, which can even result in sudden cardiac arrest. This disease is often misdiagnosed as dilated or ischemic

cardiomyopathy, apical hypertrophic cardiomyopathy, or other myocardial infiltrative processes, including tumors. The goal of this

article is to provide an updated and detailed overview of the isolated form of LVNC.

Keywords: non-compaction cardiomyopathy, heart failure, trabecularization, echocardiography, cardiomyopathy

Published: December 1, 2015  Show citation

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Skopoulis S, Suková N, Frídl P, Karimova Z. Isolated form of left ventricular non compaction cardiomyopathy (LVNC) as a rare cause of heart failure. Interv Akut Kardiol. 2015;14(4):154-157.
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